Pathways of ammonia detoxification to GLN in muscles linked to Increased use on the BCAA and ?-KG (cataplerosis) and suggested results of BCAA and phenylbutyrate in subjects with liver cirrhosis or UCD. Optimistic influence of BCAA on ammonia detoxification to GLN might be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbuty